Lenalidomide, bortezomib and dexamethasone has
notable activity in the frontline treatment of
myeloma, including patients with high risk disease
Pl
Paul Ri
Ri h
c ard
1
dson, SL
Sagar L
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on l 2
al, Ad
And
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rze J kb
akubowi k
3
ak, SdJ
Sundar J
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aganna h
4
th, Noopur
Raje,
5 David Avigan,6 Irene Ghobrial,1 Robert Schlossman,1 Amitabha Mazumder,4 Nikhil
Munshi,
1 David Vesole,4 Robin Joyce,6 Deborah Doss,1 Diane Warren,1 Laura Lunde,1
Rachel Lukas,
1 Sarah Kaster ,5 Kathleen Shea ,5 Carol Delaney,6 Marisa Lauria,6
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Const
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tine Mit
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ades, TH
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Rob t
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Kenneth Anderson
1
1
Dana-Farber Cancer Institute, Boston, MA; 2Winship Cancer Institute, Atlanta, GA; 3University of
Michigan Comprehensive Cancer Center, Michigan, MI;
4St. Vincent's Comprehensive Cancer Center,
New York, NY;
5Massachusetts General Hospital, Boston, MA; 6Beth Israel Deaconess Medical Center,
Boston, MA;
7Celgene, Inc., Summit, NJ and 8Millennium Pharmaceuticals, Inc., Cambridge, MA.

Background
g
ˇ Bortezomib (Bz) as a single agent
1,2 and lenalidomide
(Len)
() plus
p
dexamethasone (Dex
(
)
3,4
)
are approved
pp
treatments for relapsed multiple myeloma (MM) pts who
have received 1 prior therapy
Ph III
d
ran
i
om zed st di
u es confirmed superiority of
Bz
1,2 and Len/Dex3,4 versus high-dose Dex alone
ˇ Bz is also approved
pp
for the treatment of newly
diagnosed MM pts
5
ˇ Bz/Dex
6-8 and Len/Dex9,10 are active in frontline MM
1.
Richardson, et al. N Engl J Med 2005;352:2487-98.
6.
Jagannath, et al. Blood 2006;108:238-9a (abstract).
2.
Richardson, et al. Blood 2007;110:3557­60.
7.
Harousseau, et al. Haematologica 2006;91:14981505.
3.
Weber, et al. N Engl J Med 2007;357:2133-42.
8.
Harousseau, et al. J Clin Oncol 2008;26: 455s, Updated
4.
Dimopoulos, et al. N Engl J Med 2007;357:2123-
data presented at ASH2008 joint ASH-ASCO symposium.
2132.
9.
Rajkumar, et al. J Clin Oncol 2008;26:2171-2177.
5.
San Miguel, et al N Engl J Med 2008;359:906-17.
10. Lacy, et al. Mayo Clin Proc 2007;82:1179-84.

Rationale for Combination Therapy
in Multiple Myeloma
IMiDs, Bortezomib
Dex
Bortezomib
Alkylators
Anthracyclines
Mitochondria
NF-B
Cytochrome-c
Smac
Caspase-8
Caspase 9
Caspase-
Caspase 3
PARP
Tumor cell death
Tumor cell death
From Richardson PG , Mitsiades CS, Hideshima T, Anderson KC: Expert Review of AntiCancer Therapy. 2008;8:1053.

Background and Study
gy Aims
ˇ
Pre-clinical studies suggest synergy of Len and Bz
1
ˇ
Ph II study of Len/Bz/Dex in relapsed/refractory MM pts
2
yp
y
p
84% response rate (MR or better), including 68%
CR/nCR+VGPR+PR
Len/Bz/Dex well tolerated with
with only 1 pt with G3 peripheral
neuropathy (PNY) and 2 pts with deep vein thrombosis
(DVT)
Dd
Dex dose
d
re
t
uc i
tion was
i
requ red in 14
14 t
p s leadi
ding to
protocol amendment, using lower dose of Dex (20 mg)
ˇ
Update efficacy and ASCT data from the Ph l/ll study of
3
Len/Bz/Dex in frontline MM pts, including response in high-risk
pts
1.
Mitsiades, et al. Blood 2002;99:452­530.
2.
Richardson, et al. ASH 2008; Abstract 1742.
3.
Richardson, et al. J Clin Oncol 2008;26:Abstract 8520.

Objectives
ˇ
Primary:
Define maximum tolerated dose (MTD) of Len/Bz/Dex
Response rate (CR+
(CR PR)
PR)
ˇ
Secondary:
CR+PR after
after 4 and 8 cycles
CR+nCR rate
TTP, DOR, PFS and OS
Ti
Toxi i
c t
ity
Surrogate markers
Cytogenetic analysis, gene expression profiling (GEP)
ˇ
Pts proceeding to ASCT:
Stem cell data (# CD34+ cells,
(, # days
y of harvest,
mobilization strategies)
Engraftment parameters

Patients
ˇ
Inclusion criteria:
Newly diagnosed
yg
MM
No previous systemic MM therapy (bisphosphonates
permitted)
Prior radiotherapy
radiotherapy completed
completed 2 wks
wks before study entry
Karnofsky performance score
(KPS) 60%
ˇ
Exclusion criteria:
Concomitant corticosteroids
PNY G2 (NCI CTCAE v3.0)
Renal insufficiency (sCr >2.5 mg/dL)
Platelets <50,000 cells/mm
3
ANC <1,000 cells/mm
3
Hemoglobin <8.0 g/dL
gg
AST/ALT 2 × ULN

Study Design
Up to eight 21-day cycles*
1 2
4 5
8 9
11 12
14
21
Bz
Bz
Bz
Bz
Dex
Dex
Dex
Dex
Lenalidomide
*Dex, 40 mg/day days 1, 2, 4, 5, 8, 9, 11, and 12; 20 mg, cycles 5­8;
amended to 20 mg/10 mg cycles 1­4/5­8 based on safety data
ˇ
Pts PR may proceed to ASCT after 4l
4 cycles
ˇ
After 8 cycles, maintenance therapy permitted in responding
pts using wkly ( D1, 8) schedule of Bz and Dex on D1, 2, 8,
and 9
ˇ
Antithrombotic therapy with daily aspirin (81 or 325 mg)
ˇ
Antiviral therapy as prophylaxis against Herpes Zoster

Phase I Dose
Dose Levels
Levels
Dose level*
Len
Bz
Dex**
1
15 mg/day
1.0 mg/m
2
40 mg
2
15 mg/day
1.3 mg/m
2
40 mg
3
20 mg/day
1.3 mg/m
2
40 mg
4
25 mg/day
1.3 mg/m
2
40 mg
4M
25 mg/day
1.3 mg/m
2
20 mg
*An additional dose level (DL) introduced based on safety data;
20 mg Dex, cycles 1­4, and 10 mg Dex, cycles 5­8 (DL 4M)
**40 mg, cycles 1­4; 20 mg, cycles 5­8 (DL 1-4)

Patient Accrual
Accrual
Phase I
ˇ
Successive cohorts of 3­6 pts per dose level
ˇ
Dose escalation proceeded depending on dose-limiting
toxicities (DLTs):
G3 non-hematologic toxicity
G4 thrombocytopenia with platelets <10,000/mm
3 on
>1 occasion despite transfusion support
G4 neutropenia for >5 days and/or resulting
yg in
neutropenic fever
Inability to receive cycle 2 day 1 dose due to drug-related
toxicity
ˇ
MTD: dose level prior to that resulting in 2 DLTs
10 additional pts to be enrolled at the MTD
Phase II
ˇ
35 pts to be enrolled at MTD or maximum planned dose (MPD)

Assessments
ˇ Toxicities graded by
gy NCI CTCAE v3.0
ˇ Responses assessed by modified EBMT criteria
1,2
and Uniform Criteria (UC)
3
() (to include VGPR)
()
ˇ After cycle 2, then after every cycle
ˇ Response assessments for evaluable pts were
confirmed by 2 assessments, 6 wks apart as per
modified EBMT criteria
1.
Bladé ,et al. Br J Haematol 1998;102:1115-23.
2.
Richardson, et al. N Engl J Med 2003;348:2609-17.
3.
Durie, et al. Leukemia 2006;20:1467-73.

Baseline Characteristics
Characteristics ­ Phase I/II
Characteristics
N=66*
N=66
Median age, years (range)
58 (22­86)
Male, n (%)
36 (55)
Myeloma type, n (%)
IgG
44 (67)
IgA
14 (26)
light-chain
2 (4)
light-chain
1 (2)
ISS stage II/III at diagnosis, n (%)
33 (50)
Durie-Salmon stage II/III at diagnosis**, n (%)
41 (65)
* 68 pts enrolled; 2 pts with data pending
** Data based on 63 of 66 pts with available data

Disposition ­ Phase I & ll (N=68)*
ˇ Ph I and ll enrollment is complete
Phase l enrollment
N=33
Dose level 1
3
Dose level 2
3
Dose level 3
4**
Dl
Dose l
l
eve 4
6
Dose level 4M
17
Phase ll
ll
enro
t
men
N3
N= 5
35
*as of November 2008
**1 pt did not receive treatment; not included in MTD determination

Phase I ­ DLTs and MTD
MTD
ˇ Two DLTs seen at dose level 4:
G3 h
l
yperg ycemia* due to hi h
g dD
-dose Dex
ˇ MPD has been reached at dose level 4M:
Len 25 mg
Bz 1 3 mg/m
2
Bz 1.3 mg/m
Dex 20 mg
*G3 hyperglycemia defined by NCI CTCAE v3.0 as serum glucose levels of
>250­500 mg/dL (>13.9­27.8 mmol/L)

Treatment and disposition
to d t
a e (
66)
n=
ˇ Median treatment duration: 9 cycles (range 2­35)
Completed 8 cycles
46 (70%)
Proceeded to ASCT
15 (23%)
Pt choice (prior to completion)
3
PD
5
Discontinuation 2ary to PN
2
ˇ Dose reductions:
Len in 18 pts
Bz in 26 pts
Dex in 35 pts

Most Common Toxicities G3/4
DVT
Pneumonia
G3
Chest pain
G4
Neuropathy
Mental status
Dizziness
Metabolic
Renal
Liver
Infection
Insomnia
Cardiac
Thrombocyto...
Neutropenia
Lymphopenia
Leukopenia
Anemia
024
68
ˇ
Toxicities have been manageable:
Pts, n
ˇ
all G3/4 hematologic toxicities (
g(3­15%)
ˇ
G3 hypophosphatemia (8%)
ˇ
G2-4 DVT/pulmonary embolism ( n=3, 4%)
ˇ
G3 PNY (3%)
ˇ
no treatment-related mortality

Overall Response
Response Rate
Rate (n=
(n 65)
ˇ Best response* (EBMT/UC) in 65 evaluable pts:
20 CR
(31%)
6 nCR (9%)
39 PR (60%)
- 23 VGPR (35%)
ˇ Overall response rate, PR: 100%
ˇ VGPR: 75%
ˇ CR/nCR: 40%
* As of Feb 2009

Best Response ­ By Phase/Cohort
Response-evaluable
Dose level
CR
nCR
VGPR
PR
MR
pts
Phase I
31
7 (23%)
1 (3%)
14 (45%)
9 (29%)
0 (0%)
13
1
1
1
23
2
1
33
1
0
2
4
6
1
032
4M
16
2
0
9
5
Phase II
34
13 (38%)
5 (15%)
9 (26%)
7 (21%)
0 (0%)
TOTA
T L
65
20 (31%)
6(
6 9%)
(9%)
23 (35%) 16 (25%)
0(
0 0%)
(0%)
ˇ Duration of response for pts with confirmed best response;
Md
Me i
dian: 2 8
. mos (range 1 4
. 25
­
6
.
)
mos *
)*
* As of Nov 2008

Response Independent of Baseline
Cytogenetics or ISS Stage
Stage
No
With
Normal
Abnormal
No t(4;14)
With t(4;14)
Del 13q
Del 13q
n*
39
23
51
7
48
10
PR
100%
100%
100%
100%
100%
100%
P
0.108
0.454
.757
VGPR
72%
83%
75%
71%
73%
80%
P
0.337
.861
.642
ISS I
ISS II
ISS III
n*
33
22
9
PR
100%
100%
100%
P
0.368
VGPR
85%
64%
78%
P
0.926
*pts with available data, as of Feb 2009

Time to event (TTE) and
and SCT data
data
ˇ After median follow-up of 8 mos:
Median TTP, PFS, and OS have not yet been
reached
ˇ Stem cell collection has proceeded successfully
in 21/23 pts:
p
Median 6.2 x 10
6 CD34+ cells after a median
of 6 cycles of therapy
15 pts have proceeded to ASCT, with
unremarkable transplant
p
course

Conclusions
ˇ Len/Bz/Dex produces high-quality, durable
responses and is well tolerated in newly
py
diagnosed MM pts, irrespective of cytogenetic
status or ISS stage
ORR 100% across all
all cohorts and at
at MPD
MPD
ˇ MPD established: Len 25 mg, Bz 1.3 mg/m
2, Dex
20 mg
ˇ Toxicities manageable ­ 2 pts with G3 PNY (3%)
and 3 pts with DVT (4%)
ˇ Stem cell mobilization has been successful in
almost all pts, with transplant course
unremarkable to date

Future Directions
ˇ Additional analyses are under way for:
ˇ Time to events
ˇ Cytogenetics
ˇ Proteomics
ˇ Gene expression profiling
ˇ Mobilization strategies
ˇ Further Phase 3 studies
studies of RVD are
are in process and/or
planned (with or without ASCT)
ˇ Addition of other agents (e
g( g CRVD, RVDD, RVD + SAHA)
as part of Phase I/II trials ongoing

Acknowledgments
ˇ Dana-Farber Cancer Institute
ˇ Winship Cancer Institute
ˇ University of Michigan Comprehensive
Cancer Center
ˇ St Vincent's Comprehensive Cancer Center
ˇ Massachusetts General Hospital
ˇ Beth Israel Deaconess Medical Center
ˇ Research nurses, coordinators, and other
staff at
at all
all study sites
ˇ Celgene Corporation
ˇ Millennium
u
Pharmaceutica
cals,
s, Inc.
ˇ The patients and their families